Home > E. Pathology by systems > Respiratory system > Lungs > interstitial lung diseases

interstitial lung diseases

Monday 1 March 2004

Digital case

- JRC:6465 : hytrast crystalline pneumonitis.

Types

- drug-induced lung diseases
- environmental lung diseases and occupational lung diseases

  • pneumoconioses
  • hypersensitivity pneumonitis

- idiopathic interstitial pneumonias (IIP)

  • usual interstitial pneumonia (UIP) (idiopathic pulmonary fibrosis)
  • nonspecific interstitial pneumonia (NSIP)
  • cryptogenic organizing pneumonia (idiopathic BOOP)
  • actute interstitial pneumonia (AIP)
  • respiratory bronchiolitis-associated lung disease (RBLD)
  • desquamative interstitial pneumonia (DIP)
  • lymphocytic interstitial pneumonia (LIP)
  • neonatal interstitial pneumonia

- diffuse alveolar damage (DAD)

- chronic manifestations of systemic dysimmune syndromes (collagen vascular diseases and inflammatory bowel diseases)

  • rheumatoid arthritis
  • progressive systemic sclerosis
  • systemic lupus erythematosus
  • polymyositis/dermatomyositis
  • Sj√∂gren syndrome
  • pulmonary Crohn disease

- diffuse eosinophilic lung disease
- drug associated diffuse lung disease
- miscellaneous diffuse lung diseases

  • sarcoidosis
  • pulmonary Langerhans cell histiocytosis
  • Erheim-CHester disease
  • systemic juvenile xanthogranulomatosis
  • lymphangioleiomyomatosis
  • Hermansky-Pudlak syndrome
  • pulmonary alveolar microlithiasis
  • pulmnary alveolar proteinosis
  • lymphangitic carcinomatosis
  • chronic pulmonary aspiration
  • pulmonary vasculitis

Lesional patterns

- diffuse lung diseases with granulomas

  • sarcoidosis
  • chronic berylliosis
  • hypersensitivity pneumonitis (extrinsic allergic alveolitis)