Home > E. Pathology by systems > Skin > cylindromatosis
cylindromatosis
Wednesday 25 May 2016
WKPD |
Definition: Cylindroma is a variant of eccrine spiradenoma which can be multiple on the scalp and can coalesce to form a "turban tumour ".
Etiology
Brooke-Spiegler syndrome or familial cylindromatosis
- CYLD germline mutations
Images
cutaneous cylindroma
- https://twitter.com/mariaramir/status/731872921245863937
- https://twitter.com/JJSpeiserMD/status/739831562066333697
- https://twitter.com/proVZero/status/692375059479027713
See also
dermal eccrine cylindroma
adenoid cystic carcinoma
See also
cutaneous apocrine tumors