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composite adrenal medullary tumor

Friday 2 March 2012

composite adrenal medullary neoplasms; Composite adrenal pheochromocytoma; composite adrenal medullary tumors

Definition: Composite adrenal medullary tumors is a rare adrenal tumor composed of ordinary pheochromocytoma and other components, most frequently neuroblastic elements.

Little is known about its biologic potential, therefore creating a clinical dilemma on diagnosis.

Composite pheochromocytoma may be regarded as a histologic variant of classic pheochromocytoma.

Composite adrenal medullary neoplasms are rare entities that are composed in part of a pheochromocytoma, one of the three patterns of the neuroblastic tumors or a peripheral nerve sheath neoplasm.

Most of these tumors have been reported in adults, but have been infre-quently observed in children.

See also

- composite pheochromocytoma-ganglioneuroma tumor


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- Kragel PJ, Johnston CA. Pheochromocytoma-ganglioneuroma of the adrenal. Arch Pathol Lab Med. 1985;109:470-472.