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osteopathia striata

Friday 2 March 2012

Voorhoeve disease

Osteopathia striata is a rare benign, asymptomatic disorder characterized radio graphically by symmetrical, axially oriented, dense striations in the metaphysis of long bone.

Its presence in association with sclerosis of the base of the skull has been determined to be genetically transmitted as an autosomal dominant condition.

Osteopathia striata may be seen in association with osteopoikilosis or melorheostosis, or both, in which case the condition is usually referred to as mixed sclerosing bone dystrophy.

Many bone islands as well as evidence of melorheostosis can be seen in radiograph. This rare pattern of "mixed sclerosing bone dystrophy" is generalized throughout the skeleton.

See also

- bone-forming tumors