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sporadic renal hemangioblastoma

Wednesday 24 November 2010

Hemangioblastoma is a benign tumor that can occur sporadically, or in association with von Hippel-Lindau disease in approximately one-quarter of the cases. Only exceptionally does it occur outside the central nervous system.

Sporadic renal hemangioblastoma can be mistaken for various malignancies such as renal cell carcinoma, epithelioid angiomyolipoma, adrenal cortical carcinoma, and paraganglioma, deserves wider recognition for its occurrence as a primary renal tumor.

References

- Sporadic hemangioblastoma of the kidney: an underrecognized pseudomalignant tumor? Ip YT, Yuan JQ, Cheung H, Chan JK. Am J Surg Pathol. 2010 Nov;34(11):1695-700. PMID: 20924277