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juvenile aponeurotic fibroma

jeudi 25 mars 2010

Juvenile aponeurotic fibromatosis was first described by Keasbey. The lesion tends to occur in older children with a relatively wide age range (2.5–9 years) reported and even occasionally in adults.

Although this lesion was originally called juvenile aponeurotic fibroma, a number of other terms have been used to describe it. The most commonly accepted name is juvenile aponeurotic fibromatosis or, since the lesion may occasionally occur in adults, calcifying aponeurotic fibroma.

The histologic hallmark is calcifications seen in conjunction with an otherwise unremarkable fibrosing disease. Stippled calcification may be visible radiographically. Nuclei are large and darkly staining. Calcification may not necessarily occur in younger infants.

These lesions classically occur on the fingers and palm but may arise in relation to tendons. A recurrence rate of more than 50% is reported after resection.