VHL-associated epididymal cyst
Monday 8 March 2010
In patients with von Hippel-Lindau disease (VHL), epididymal cysts are characteristically limited to the efferent ductules.
VHL-associated epididymal cysts have a peculiar morphology with predominance of clear cells, and often evolve into cystadenomas. They are usually diagnosed in adult patients, with no evidence of congenital lesions.
Progression of epididymal maldevelopment into hamartoma-like neoplasia in VHL disease.
VHL-associated epididymal cystadenoma
Mehta GU, Shively SB, Duong H, Tran MG, Moncrief TJ, Smith JH, Li J, Edwards NA, Lonser RR, Zhuang Z, Merrill MJ, Raffeld M, Maxwell PH, Oldfield EH, Vortmeyer AO. Neoplasia. 2008 Oct;10(10):1146-53. PMID: 18813354