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extralobar pulmonary sequestration

Wednesday 29 October 2003

extra-pulmonary sequestration ; ELPS

Definition: Extralobar pulmonary sequestration (ELPS) are segmentsof lung tissue ("accessory lungs") with a distinct pleural investment and complete anatomic and physiologic seprartion from the normal lung. Blood supply is usually by anomalous systemic artery with venous drainage into the azygos or hemizygos system.

The abnormal tissue may be located either above or below the diaphragm, most often on the left side.


- Extrapulmonary sequestration w/ perfect anomalous penetrating pleural vessel. Histology shows malpositioned large vessels.

Digital cases

- HPC:413 : Cystic congenital adenomatoid malformation in extralobar pulmonary sequestration


- right extralobar pulmonary sequestration (10%)
- left extralobar pulmonary sequestration (90%)
- infradiaphragmatic extralobar pulmonary sequestration


- bronchopulmonary sequestration supplied from the renal artery (2326448)


- congenital cystic adenomatoid malformation (CCAM) (10441623)

  • inside CCAM
  • outside CCAM

- renal anomalies

- diaphragmatic hernia

- malformative syndrome

  • association anomalous pulmonary venous return, pulmonary sequestration, bronchial atresia, aplastic right upper lobe, pericardial defect and intrathoracic kidney (5944198)

Case records

- Case 10460

See also

- thoracic malformations
- pulmonary malformations