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meningioangiomatosis

Sunday 28 January 2007

Meningioangiomatosis (MA) is a rare lesion, probably of malformative origin, consisting of meningovascular proliferation and leptomeningeal calcification.

Patients with MA usually present with seizures or persistent headaches.

A neurofibromatosis type 1 (NF1) may be associated in a variable proportion of patients, while in others it may be sporadic. Surgical treatment is usually recommended, and is gratifying in most cases.

Rarely, MA has been described coexisting with meningiomas, arteriovenous malformations, encephaloceles, oligodendrogliomas, meningeal haemangiopericytomas and orbital erosion.

Among these, meningiomatosis with meningioma is the most frequent combination.

Complications (Examples)

- sudden death (15803213)

See also

- meningeal tumors

References

- Deb P, Gupta A, Sharma MC, Gaikwad S, Singh VP, Sarkar C. Meningioangiomatosis with meningioma: an uncommon association of a rare entity—report of a case and review of the literature. Childs Nerv Syst. 2006 Jan;22(1):78-83. PMID: 16389566

- Insights into meningioangiomatosis with and without meningioma: a clinicopathologic and genetic series of 24 cases with review of the literature. Perry A, Kurtkaya-Yapicier O, Scheithauer BW, Robinson S, Prayson RA, Kleinschmidt-DeMasters BK, Stemmer-Rachamimov AO, Gutmann DH. Brain Pathol. 2005 Jan;15(1):55-65. PMID: 15779237