Human pathology

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metabolic cardiomyopathies

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Types

- endocrine cardiomyopathies

- familial storage disease

  • hemochromatosis
  • glycogen storage diseases (glycogenoses)
  • Hurler syndrome
  • Refsum syndrome
  • Niemann-Pick disease
  • Fabry-Anderson disease
  • Morquio-Ullrich disease

- fatty acid oxidation diseases
- electrolytic anomalies

  • disturbances of potassium metabolism
  • magnesium deficiency

- nutritional disorders

  • kwashiorkor
  • anemia
  • beri-beri
  • selenium deficiency

References

- Gilbert-Barness E. Metabolic cardiomyopathy and conduction system defects in children. Ann Clin Lab Sci. 2004 Winter;34(1):15-34. PMID: 15038665