Human pathology

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isolated congenital asplenia

MIM.271400

familial asplenia, isolated congenital hyposplenia, familial hyposplenia, familial splenic hypoplasia

Types

- recessive
- dominant

See alos

- splenic hypoplasia
- overwhelming sepsis

  • fulminant haemophilus influenzae
  • fulminant pneumococcal sepsis

- adrenal hemorrhages
- asplenia (absence of the spleen)
- Howell-Jolly bodies in the peripheral blood
- Heinz bodies in the peripheral blood

See also

- asplenia