Human pathology

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hepatic ARPKD

MIM.263200

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Ductal plate malformation (Congenital hepatic fibrosis) in hepatic (...) Ductal plate malformation (Congenital hepatic fibrosis) in hepatic (...) Ductal plate malformation (Congenital hepatic fibrosis) in hepatic (...) Ductal plate malformation (Congenital hepatic fibrosis) in hepatic (...) Ductal plate malformation (Congenital hepatic fibrosis) in hepatic (...) Congenital hepatic fibrosis in hepatic ARPKD Liver ARPKD at 21 weeks

Synopsis

- anomalies of hepatic organogenesis (hepatic dysplasia)

Associations

- phosphomannose isomerase deficiency (10963387)
- hereditary hemorrhagic telangiectasia (9500780)

References

- Strayer DS, Kissane JM. Dysplasia of the kidneys, liver, and pancreas: report of a variant of Ivemark’s syndrome. Hum Pathol. 1979 Mar;10(2):228-34. PMID: 422192

Keywords