Human pathology

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gamma-hydroxybutyric aciduria

MIM.271980 6p22

deficiency of succinic semialdehyde dehydrogenase, SSADH deficiency
Succinic semialdehyde dehydrogenase (SSADH deficiency) (MIM 271980) is a defect in gamma-aminobutyric acid catabolism, resulting in the accumulation of gamma-hydroxybutyric acid (GHB) and causing neurological and cognitive disorders of varying severity.