IgG4-associated autoimmune pancreatitis
Autoimmune pancreatitis (AIP) has been recognized as a distinct entity with typical histopathological and immunological findings.
Autoimmune pancreatitis (AIP) is a mass-forming chronic fibroinflammatory condition centered on the pancreatobiliary system and characterized by predominant immunoglobulin G4 (IgG4)-positive plasma cells. Recent reports have brought to light the multiorgan involvement of this disease (IgG4 syndrome or IgG4 disease).
Associations
- Sjogren syndrome
- sclerosing extra-hepatic cholangitis
- retroperitoneal fibrosis
See also
hyper-IgG4 syndrome
References
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