Human pathology

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adrenoleukodystrophies

Types

- X-linked adrenoleukodystrophy (MIM.300100) (ABCD1 at Xq28)
- autosomal neonatal adrenoleukodystrophy (MIM.202370)

  • Locus 22q11
  • Locus Chr.1
  • Locus 12p13.3
  • Locus 7q21-q22
  • Locus 2p15

Videos

- Adrenoleukodystrophy by Washington Deceit

References

- Chemke J, Livni N, Rosenmann E. Adrenoleukodystrophy: evidence for cytoplasmic inclusions in white blood cells. Pediatr Pathol. 1986;6(2-3):173-9. PMID: 3029738

- Applegarth DA, Dimmick JE. Adrenoleukodystrophy, cerebrohepatorenal syndrome (Zellweger syndrome), and peroxisomes. Pediatr Pathol. 1985;3(2-4):377-8. PMID: 4095031

- Powers JM, Moser HW, Moser AB, Schaumburg HH. Fetal adrenoleukodystrophy: the significance of pathologic lesions in adrenal gland and testis. Hum Pathol. 1982 Nov;13(11):1013-9. PMID: 6759362